Anemia sideropenica [show article only]hover over links in text for more info . La disfagia e la glossite in questi casi sono sostenute appunto da una distrofia. Disfagia [show article only]hover over links in text for more info Disfagia sideropenica, attualmente meglio conosciuta come Sindrome di Plummer-Vinson . La sindrome di Plummer-Vinson (detta anche PVS, disfagia sideropenica, o sindrome di Patterson-Kelly) è costituita dalla triade clinica di disfagia, anemia.
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MEDCICLOPEDIA: DICCIONARIO ILUSTRADO DE TÉRMINOS MÉDICOS
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Only comments written in English can be processed. Plummer-Vinson or Paterson-Kelly syndrome presents as a classical triad of dysphagia, iron-deficiency anemia and esophageal webs. Exact data about the sideropeniica of the syndrome are not available; the syndrome is extremely rare.
Most of the patients are white middle-aged women, in the fourth to seventh decade of life, but the syndrome has also been described in children and adolescents. The dysphagia is usually painless and intermittent or progressive over years, limited to solids and sometimes associated with weight loss.
Symptoms resulting from anemia weakness, pallor, fatigue, tachycardia may dominate the clinical picture. siderooenica
Additional features are glossitis, angular cheilitis and koilonychia. Enlargement of the spleen and disfayia may also be observed. One of the most important clinical aspects of Plummer-Vinson syndrome is the association with upper alimentary tract cancers. The etiopathogenesis of Plummer-Vinson syndrome is unknown. The most important possible etiological factor is iron deficiency.
Other possible factors include malnutrition, genetic predisposition or autoimmune processes. Plummer-Vinson syndrome can be treated effectively with iron supplementation and mechanical dilation. In case of significant obstruction of the esophageal lumen by esophageal web and persistent dysphagia despite iron supplementation, rupture and dilation of the web are necessary.
Since Plummer-Vinson syndrome is associated with an increased risk of squamous cell carcinoma of the pharynx and the esophagus, the patients should be followed closely.
Other search option s Alphabetical list. Summary and related texts. Check this box if you wish to receive a copy of your message. Disease definition Plummer-Vinson or Paterson-Kelly syndrome presents as a classical triad of dysphagia, iron-deficiency anemia and esophageal webs. Kelly-Paterson syndrome Sideropenic dysphagia Prevalence: Summary Epidemiology Exact data about diisfagia epidemiology of the syndrome are not available; the syndrome is extremely rare.
Clinical description Most of the patients are white middle-aged women, in the fourth to seventh decade of life, but the syndrome has also been described in children and adolescents. Etiology The etiopathogenesis of Plummer-Vinson syndrome is sideropehica.
Management and treatment Plummer-Vinson syndrome can be treated effectively with iron supplementation and mechanical dilation. Detailed information Professionals Review article Disfagka Additional information Further information on this disease Classification s 2 Gene s 0 Clinical signs and symptoms Publications in PubMed Other website s 2.
Health care resources for this disease Expert centres Diagnostic tests 0 Patient organisations 1 Orphan drug s 0.
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